Trombotické mikroangiopatie – dostupnost diagnostických metod a léčebných možností v ČR v roce 2021

Výsledky syndikovaného průzkumu mezi klinickými hematology

Authors

  • Jaromír Gumulec Klinika hematoonkologie FN Ostrava
  • Miriam Lánská IV. interní hematologická klinika Fakultní nemocnice Hradec Králové
  • Ingrid Hrachovinová Ústav hematologie a krevní transfuze Praha
  • Peter Salaj Ústav hematologie a krevní transfuze Praha
  • Zdeněk Kořístek Klinika hematoonkologie Fakultní nemocnice Ostrava a Lékařské fakulty Ostravské university
  • Ivo Demel Klinika hematoonkologie Fakultní nemocnice Ostrava
  • David Buffa Klinika hematoonkologie Fakultní nemocnice Ostrava
  • Lucie Broskevičová Klinika hematoonkologie Fakultní nemocnice Ostrava
  • Martin Pulcer Ústav laboratorní medicíny Fakultní nemocnice Ostrava a Lékařské fakulty Ostravské univerzity
  • Petra Kovářová Krevní centrum Fakultní nemocnice Ostrava
  • Jan Martinek Oddělení imunologie a alergologie, Zdravotní ústav se sídlem v Ostravě
  • Pavel Žák IV. interní hematologická klinika Fakultní nemocnice Hradec Králové

Keywords:

thrombotic microangiopathies, thrombotic thrombocytopenic purpura, haemolytic-uremic syndrome, HELLP syndrome, archiving of biological material, exchange plasmapheresis, ADAMTS13, PLASMIC score, French score

Abstract

From September to October 2021, at the request of the Centre for Thrombotic Microangiopathies Ostrava (C4TMO) and the Czech Group for Thrombotic Microangiopathies (CS4TMA), an online survey prepared by IQVIA based on CS4TMA data was conducted among clinical haematologists to verify the awareness of clinical haematologists about the rules and availability of care for patients with thrombotic microangiopathies. The professional basis for the development of the question set was the formulation of good clinical practice guidelines for the care of patients with thrombotic thrombocytopenic purpura. A total of 49 interviews were conducted. The results of the survey indicate very good clinical practice for the care of patients with acute TMA at the respondents' workplaces. However, the spectrum of departments that participated in the survey does not correspond to the actual spectrum of haematology departments in the Czech Republic. In particular, data from small outpatient clinics within type II hospitals or outside hospitals are missing.

Published

2023-12-18