Outcome of a patient with Herlyn-Werner-Wunderlich syndrome treated with Balloon septostomy – pre- and postsurgical ultrasound findings

Abstract

Herlyn-Werner-Wunderlich syndrome is an unusual congenital anomaly defined by a triad of congenital defects of female urogenital tract – homolateral renal agenesis, uterus duplex and obstructed hemihematometrocolpos which etiology remains still unclear. Pelvic pain, dysmenorrhea and palpable mass due to the hematocolpos or hematometra are the most common clinical symptoms. Due to the recent studies endometriosis is considered to be prevalent finding in these young patients possibly explaining the pathophysiological mechanism of endometriosis as the result of retrograde menstruation. Early diagnosis and subsequent treatment are important to prevent the development of severe complications. In general, clinical and reproductive outcomes after drainage of the hematometrocolpos are reported to be satisfactory. We present the 13 year old patient presented with the pelvic pain and diagnosed with OHVIRA syndrome treated with Balloon septostomy.